Mauriac syndrome mu shuga

Mauriac syndrome - matenda kuti umakula Vuto ndi chifukwa mankhwala molakwika shuga ali mwana. Kwa nthawi yoyamba matendawa limafotokonzera 1930 ndi French dokotala Pierre Mauriac chiyambi. Iye anafotokoza mtundu wa chithunzi matenda imene ana akudwala matenda a shuga ndi mankhwala insulin zapitazi mlingo cholakwika, kusonyeza zizindikiro kunja. Anaona kuti ana onse ofanana mu maonekedwe, kumene munthu amasonyeza mwa kukula, kunenepa, kupepera chitukuko otsika kugonana.

Zimayambitsa matenda

Chifukwa chachikulu cha mavuto aakulu sizolondola anathamangitsa shuga mankhwala. Mu matenda kapamba si zikugwira ntchito bwino, wosapatsa zedi okwanira insulin. Chifukwa kudwala kumachitika shuga akusowa mu maselo chifukwa chakuti kuti limafotokoza zambiri m'magazi.

Mauriac syndrome chitukuko odwala matenda a shuga Chingelezi mtundu 1 amagwirizana ndi chithandizo kuchepa. Odwala mwana kwa nthawi yaitali osakwanira insulin mlingo kutumikiridwa, kapena ntchito mankhwala a khalidwe otsika ndi zoipa ayeretsedwe, kutsogolera ku akusowa aakulu a insulin.

Yaitali kupanda insulin m'thupi kumayambitsa njira zotsatirazi:

• matenda kagayidwe kachakudya, makamaka matenda zimam'patsa kagayidwe.
• Kukula kukula kwa chiwindi ndi mafuta ake alibe chifukwa kuchuluka glycogen kusokonezeka.
• Kusintha magazi zikuchokera - kuwonjezeka shuga magazi, mafuta, mafuta zidulo.

Ngati izi si njira zonse pathological mu thupi pa matenda Mauriac, komanso odwala Dokotala kuona zolakwika zotsatirazi:

• Osakwanira ulimi wa mahomoni zofunika - tochepa, kukula timadzi, glucagon, ndipo monga chotsatira cha kuphwanya kakulidwe.
• Kusokonekera kwa mapuloteni ndi wolemera linanena bungwe kashiamu ndi phosphorous pa mafupa, kenako wopita ku chitukuko cha kufooka kwa mafupa ndi ena manja minofu.
• Kulephera mayamwidwe a mavitamini mu intestine lapansi.

Matendawa zambiri kumaonekera zaka zapakati pa zaka 15-18, koma m'kati osokonekera ayamba kale kwambiri. Pakali pano, zochizira matenda ashuga oyambirira amagwiritsa zamakono bwinobwino mwayeretsa kukonzekera, omwe pafupifupi kumatha chitukuko cha matenda Mauriac.

symptomatology matendawa

Mauriac Syndrome shuga angapo matanthauzo:

• The mwana zomwe zikutsalirazi kumbuyo chitukuko ndi kukula chopinga. Nthawi zambiri pali kunenepa ndi aafupi. Pankhaniyi, mwana odwala kwanthawi kumbuyo anzawo kukula mwa 10-30 masentimita.
• The kwanthawi mu chitukuko kugonana (underdeveloped makhalidwe kugonana ndiponso kusapezeka kwa msambo atsikana).
• Protracted msinkhu.
• Kunenepa, makamaka nkhope ndi thupi chapamwamba ndi miyendo woonda. ana odwala ofanana kwambiri, ndi "kachigawo woboola pakati" pa nkhope zina, lalifupi khosi, mafuta mu manja, mapewa, pamimba. The mmunsi mwa thupi woonda kwambiri.
• Kuchuluka chiwindi limodzi wozungulira venous kufalitsidwa.
• Kufooka kwa mafupa (liwiro kukula kwa minofu fupa).
• matenda diso, kuphatikizapo matenda kwa diso, ndipo kenako chitukuko cha ng'ala.

Ambiri Mauriac syndrome ana, odwala mwana chithunzi ikusonyeza zimene zizindikiro ndi matendawa.

matenda a matenda

The matenda a "Mauriac syndrome" amamasulidwa pa zoonekeratu zizindikiro kunja matenda, monga: kupanda kutalika kwa zaka, pamaso pa kunenepa, makamaka nkhope chosakhwima kugonana, kuwonjezereka bwino mu chiwindi.

Kutsimikiza matenda ikuchitika MAGAZI zinachititsa kuti mawonetseredwe zotsatirazi:

• shuga milingo wosakhazikika, kusonyeza kudumpha nthawi zonse zazikulu, kenako pansi.
• lipids Kugwiritsa magazi (hyperlipidemia).
• A kuwonjezeka kwambiri misinkhu magazi mafuta m'thupi (hypercholesterolemia).

Nthawi zina, zina kuphunzira chiwindi biopsy Mwaichi, kuti atulutse katundu mafuta

matenda

Pakuti thupi wamng'ono matenda ndi kovuta. Monga mtundu aakulu a shuga, n'zovuta zoperewerazo. Zimayambitsa acidosis ndi hyperglycemic chikomokere.

Mauriac syndrome amapezeka aakulu chifukwa cha Kuwonjezera pafupipafupi matenda osiyanasiyana opatsirana, komanso kuchira ndondomeko zovuta yaitali amuzolengedwa mu thupi.

Mauriac syndrome ndi Nobekura: Kufanana ndi kusiyana

Mauriac syndrome ndi Nobekura zambiri akufotokozera ana, matenda onse ndi vuto lalikulu shuga kuti amapezeka pa maziko a mankhwala molakwika. Onse syndromes ndi zizindikiro zofanana, iwo monga kukula retardation ndi chitukuko cha kugonana, ndi protracted unyamata, mafuta m'chiwindi. Pankhaniyi, waukulu kusiyana Nobekura syndrome ndi kupanda thupi owonjezera mafuta. Pankhaniyi, mankhwalawa syndromes onse Cholinga zifukwa wodwala matenda a shuga.

Mauriac syndrome chithandizo

chithandizo Direct ya matenda ngati izi kulibe. mankhwala onse kuthetsa zimene zimayambitsa matenda ndi mavuto chifukwa cha iwo. Kuti tichite zimenezi, mtima ulipo kwa zolondola mankhwala insulin mu mlingo lolondola ndi khalidwe ndi mankhwala amakono.

Pofuna kupewa lipodystrophy unachitikira angapo njira zodzitetezera Mwaichi anaikidwa kukhala kutikitirako physiotherapy ndi matchati anthu jakisoni insulin. zakudya zapadera awerenge kuwonjezera mankhwala, amachotsedwa zakudya zakudya zonse munali nyama mafuta. Pankhaniyi, zakudya tikunena mapuloteni ndi zimam'patsa zakudya.

mankhwala Medical amadziwikanso cholinga azilipira kukhala pa maziko a amabweretsera mavuto matenda kwa naznachetsya izi mtima:

• Chikuonetseratu gepatoprotektorov kubwezeretsa maselo chiwindi.
• mavitamini B kubwezeretsa kagayidwe yachibadwa.
• Zovuta mankhwala umalimbana normalizing pa kaperekedwe ka lipids ndi mafuta m'thupi m'magazi.
• mankhwala steroid kwa hule kukula thupi.
• mankhwala m'thupi kubwezeretsa ntchito zofunika kugonana.

Kupewa ndi madokotala ananena zawo

Pofuna kupewa vuto yoopsa a shuga matenda Mauriac, m'pofunika kuti agwire chithandizo olondola a matenda chachikulu ndi kupewa kuperewera insulin.

Zimagwira chithandizo kale njira vuto mankhwala amakono Kulosera tsogolo la matenda yabwino zokwanira, koma ngati malangizo dokotala. Mlingo olondola a insulin ndi kubwezeretsa magwiridwe a ziwalo zonse anakhudzidwa amatha kubwerera umoyo wa mwanayo, onse kunja ndi mkati.