ThanziMatenda ndi zokwaniritsa

Lou Gehrig syndrome. Kodi kuthana ndi matenda Charcot?

Charcot ndi matenda - ndichiyani ndi kusonyeza? Kuti ife kuthera pa tsiku nkhaniyi.

Kufotokozera za matenda

Charcot Syndrome (kapena likukulira claudication) ndi matenda yodziwika ndi maonekedwe komanso kuwongola akukumana ndi mavuto malekezero m'munsi pa kuyenda. zosonyezera zimachititsa wodwalayo kusiya, chifukwa zizindikiro yekha dzina lake pafupifupi musavutike. Nthawi zambiri kukana ili la anthu ongoyendayenda chifukwa cha:

  • muyeso wa mowa ndi fodya;
  • onenepa;
  • magazi mafuta milingo;
  • chibadwa, ndi zina zotero.

Zizindikiro zazikulu

syndrome Charcot a - ichi ndi chikhalidwe ndithu zopweteka zimene amachititsa kusapeza mtima ndipo kwambiri impairs khalidwe la moyo. Ndi kukanidwa ichi munthu nthawi zambiri amadandaula za kutopa, komanso ululu komanso ululu miyendo poyenda, makamaka matako ndi minofu ng'ombe. Pali milandu kumene ululu isanafalikire mu zimakhala minofu ya ntchafu ndi m'chiuno. Monga odwala ndi matenda a matenda a Charcot kutengera mwina zatha ndipo anafooka yomweyo pambuyo mpumulo mwachidule.

Mu matenda amenewa mu wapotalikira m'munsi malekezero a wodwalayo nthawi zambiri anati trophic ndi vegetative-mtima matenda (mwachitsanzo, akrozianoz, mapazi ozizira, marbling wa khungu ndi kusintha osachiritsika, kusowa zimachitika mu mitsempha ya phazi ndi chilonda cha zala, nthawi zambiri chimafikira proximally malangizo).

Komanso, syndrome Lou Gehrig amakhala ndi kusintha osachiritsika ndi dystrophic mafupa ndi mafupa (hypertrophy a zigawo payekha, alibe wa chichereŵechereŵe, sequestrations fupa, osteophytes, intraarticular ndi mowiriza fractures mafupa yaitali). Komanso, laxity ndi kuchepetsedwa tilinazo malo kwambiri kumaonjezera ngozi ya kuvulala zoopsa.

zimayambitsa

Charcot ndi matenda - matenda chifukwa cha kugonjetsedwa kwa mitsempha mwendo (thromboangiitis, obliterans atherosclerosis, mawonekedwe zotumphukira wa aortoarteritis nonspecific ndi zina zotero.). Ululu mtima zimachitika chifukwa osakwanira otaya magazi minofu minofu wa malekezero a m'munsi. Komanso, matenda chingachitike n'chiyani psinjika za Kauda equina mu stenosis msana, osachepera - chifukwa cha msana ischemia mu arteriovenous malformation, kapena atherosclerosis kwa msempha.

mankhwala a matenda

Therapy likukulira claudication ndi ndiwo mankhwala mwachindunji za matendawa, womwe mitsempha. Childs, mu Zikatero madokotala amalangiza odwala awo kusiya makhalidwe onse oipa, kuonda ndi kutsatira zakudya kwambiri. Odwala komanso anatumizidwa akonzedwa wapadera wa thupi, kuti anakunda zizindikiro za matenda.

Koma njira ndiwofatsa mankhwala, ndiye iwo monga kulandira mankhwala osiyanasiyana. zochita zawo amapereka analgesic ndi vasodilator kwenikweni. Komanso mankhwala ndalama amathandiza kuchepetsa mafuta m'thupi m'magazi ndi dilution ake.

Wosowa pachimake kuti alowererepo opaleshoni ntchito ndondomeko yomwe lakamba zambiri za mtsempha wamagazi lumen mwa kuyambitsa mu izo catheter wapadera.

Syndrome, Charcot-Marie-Kam'nyanja matenda

kupatuka ili mukuimira munthu wa gulu la matenda tinatengera, amene yodziwika ndi alibe ulusi mitsempha zotumphukira. Tikumbukenso kuti mitundu osiyana otchedwa syndrome molungama pa zofooka zosiyana chibadwa. Ambiri mwa matenda amenewa ali tinatengera mu autosomal lalikulu limagwirira. Komabe, panopa kuzindikiridwa ndi embodiments matenda kugwirizana ndi guluu wolimba wa X khromozomu.

Mu matenda amenewa, Charcot-Marie syndrome, wodwalayo anakhudzidwa msana ndi misempha zotumphukira. Malinga ndi zenizeni majini chilema anthu akhoza kupangidwa axonal kapena demyelinating neuropathy.

Nthawi zambiri ankaimira kupatuka ndi iyamba kukhala mu unyamata kapena unyamata. Zizindikiro za gulu matenda kenako nakweza mawu ake, ndi matenda ili m'kati, limene limapezeka digiri chilungamo cha kupunduka, osati kudzetsa imfa.

Zizindikiro za kukanidwa

matenda ayamba kutuluka kuchokera wapotalikira minofu ya manja ndi kufooka kwa zimakhala mwendo. M'kupita kwa nthawi, mapazi opunduka ndi zala zazikulu ndi hammertoes. Ana ndi matenda izi pafupifupi nthawi zonse anawona kuchedwa kukula.

Chithandizo cha matenda otengera

mankhwala enieni chikhalidwe choterocho pathological kulibe. Komabe, patsogolo thanzi la odwala, Madokotala amakonda kulemba physiotherapy ndi mankhwala kuntchito. Komanso, odwala matenda izi ankagwiritsa ntchito mitundu yonse ya zipangizo zachipatala kuti kulola kuthetsa zizindikiro ululu. Mwachitsanzo, pamene mpanda phazi ntchito mafupa kulimba ikuthandizira shank ndi zina zotero. Komanso ali ndi phindu ndi lalikulu la uphungu chibadwa.

matenda Von Willebrand a

Tikumbukenso kuti matenda otengera sakuphatikizapo Charcot Syndrome. matenda Von Willebrand a akhoza kudzera mwa achibale.

Monga amadziwika, zopatuka ikuyimiridwa ndi matenda ambiri kumtundu, zikubweretsa kusokonezeka kwa coagulation magazi kapena ndondomeko clotting. Koma nthawi zambiri matendawa amapezeka mu moyo chifukwa cha matenda ena (ie anapeza mawonekedwe).

zizindikiro matenda

Chiopsezo magazi pamene kupatuka ngati n'chosiyana kwambiri malingana ndi mtundu wa matenda. Zinthu zofunika kwambiri pa matenda otengera ndi nosebleeds kobwereza, zosadziwika kufinya ndi kufinya, magazi m'kamwa, ndi zina zotero. Akazi akhale chidakwa kusamba nthawi, ndi pa kubadwa akhoza kusiya yambiri magazi.

mankhwala a matenda

Odwala matenda izi palibe mankhwala n'kofunika, koma chiopsyezo chotenga magazi ochuluka nthawi zonse ankalimbikitsa. Choncho wodwala akhoza akulimbikitsidwa mankhwala omwe kuchepetsa chizindikiro bwino matenda. Ngati wodwalayo inyamuka kuchita opaleshoni, dokotala ayenera kugwira mankhwala otetezera.

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