Adolph Strümpell Disease: Zizindikiro ndi Chithandizo

Adolph Strümpell matenda - ndi kudwala yodziwika ndi mwapang'onopang'ono kufooka mu nthambi m'munsi, ndi bwino minofu kamvekedwe mu iwo. Ndi matenda otengera kuti akhoza anapezeka pa m'badwo uliwonse kwathunthu kwa ana aang'ono kuti ukalamba akale.

mwachidule

Adolph Strümpell matenda - aakulu, matenda pang'onopang'ono kwa wamanjenje dongosolo limene limabweretsa gulu la matenda sakanikira. Iwo amakhala ndi otchedwa amgwirizano chotupa wa kapepalako pyramidal mu zapambuyo ndi zapambuyo msana. mitundu lalikulu la matenda anapanga m'zaka zingapo moyo, ndi recessive - m'tsogolo ndipo amasiyana kwambiri.

Kwa nthawi yoyamba kudwala izi anafotokoza A. Adolph Strümpell mu 1866. The katswiri anati khalidwe banja la matenda. Mu mabuku a zamankhwala pali mayina ena kudwala (Adolph Strümpell ziwalo, banja chonsechi paraplegia).

Pa matenda limanenedwa ngati pang'onopang'ono patsogolo. Mu chochitika cha pa aang'ono chikondwerero chikhalidwe zilonda. Mu nkhani ya chitukuko ina ya matenda oopsa ndipo hyperreflexia zambiri kugonjetsa matenda osiyanasiyana kuyenda. The Mapa, malinga ndi akatswiri, nyengo odwala. Mlingo wa imfa ya mphamvu yachibadwa ntchito makamaka amadalira azikhala CNS dysfunctions.

Bungwe lina gulu, Adolph Strümpell matenda (ICD-10) ndiyotengera pansi kachidindo G11.4.

The zifukwa

Zimayambitsa chenicheni cha matenda panopa osadziwika. Anthu aluso mu kufotokoza yekha malingaliro osiyana, koma palibe mmodzi wa iwo sanapezebe umboni sayansi.

matenda chibadwa

Matenda akhoza opatsirana yekha ndi motsatizana. Akatswiri onse apeza angapo mtundu wake:

• Autosomal lalikulu (mu mabanja kumene mmodzi wa makolo amadwala matenda, Mwina ndi mwana ndi matenda amenewa ali pakati pa 50 ndi 100%).
• Autosomal recessive (Mwina kubadwa kwa mwana olakwika mabanja kumene kholo lina ndi kale kudwala, kungakhale kuchokera 0 kuti 50%).
• Zogwirizana ndi X khromozomu (zambiri matenda matenda amuna).

Mu zochiritsira pali milandu wapadera (mwachitsanzo, matenda Behr, chimene kuwonetseredwa mwa manja a mitsempha chamawonedwe), pamene zizindikiro matenda kwambiri zikufanana kwambiri m'mabanja chonsechi paraplegia, koma ndi matenda osiyana.

Monga tikuonera matenda Adolph Strümpell? zizindikiro

Chitukuko cha matenda ndi mawonetseredwe a zizindikiro pang'onopang'ono. Odwala poyamba kudandaula mavuto opweteka miyendo, kumverera zonse stiffness ndi contractions convulsive. Patapita kanthawi kovuta mwendo flexion mu mafupa bondo, ndiye mtundu uwu kusintha pathological akuchuluka. Ena sangathe kutenga phazi kuchoka pansi. Komanso olumala (adzafupikitsidwa ndipo pang'ono kuposa wabwinobwino). Mu masiteji kenako pali kuswa a ntchito za ziwalo m'chiuno mwa mawonekedwe a Tisaiwale nthawi zonse kukodza.

mitundu ya matenda

Kutengera pa mbali ya kudwala panopa, zotsatirazi akalumikidzidwa ake kuima mu yochizira matenda:

• Wopepuka (chithunzi matenda odwala osakhala kufooka mu minofu ya miyendo m'munsi popanda matenda concomitant).
• Ndizovuta (kusiya zizindikiro tatchulazi odwala matenda monga malformations wa mtima, phazi chilema ndi T. D.).

Potengera kupezeka milandu anatsimikizira kwa nthendayi pakati pa achibale amadziŵika:

• matenda banja Adolph Strümpell (devolution anachita kwa makolo ndi ana).
• Idiopathic buku la matenda (mu nkhani iyi, ndi mbiri banja la matenda si wapezeka).

matenda

Ngati mwayamba nkofunika kuti kudziletsa medicate, ndipo pitani kuchipatala. Pa phwando, katswiri mu malo oyamba amatenga mbiri mankhwala wodwala, kumvetsera madandaulo ndi kufunsa mafunso (pamene panali mavuto miyendo, ngati achibale monga kudwala ndi zina zotero. D.).

Mu sitepe yotsatira, kuona ubongo. Iye akutanthauza ndi ziyenera a minofu mphamvu manja ndi miyendo, kufufuza bongo pathological. Komanso ingaperekedwe kwa kompyuta ndi maginito kumveka kulingalira za chingwe msana yokha. Phunziro lino amapereka kuphunzira kwambiri mwatsatanetsatane dongosolo ake ndi kudziwa zotheka kupatulira wa timapepala pyramidal. Dziwani kuti nthawi zambiri, CT ndi Kujambula sangosonyeza kusintha pathological.

Kodi wina otsimikiza matenda Adolph Strümpell? Matenda a matenda mulinso kuphunzira Zoyenereza imalandira. Njira imeneyi zimathandiza kuti amanena mlingo wa zikhumbo kwenikweni kuzungulira chingwe msana. Ndi kuvomerezedwa kuti ndikhale DNA mayeso kudziwa pamaso pa masinthidwe mbewu.

Ndi mwapadera tipite kwa masiyanidwe matenda, zomwe zina amayambitsa mavuto. Matendawa n'chofunika kwambiri kusiyanitsa syndrome Mills - osachiritsika chotupa cha dongosolo chapakati mantha yodziwika ndi yowonjezera ventricles ubongo ndi manja a mazunzo ndi kukwera mazunzo convolution. Kukomoka, matenda kumaonekera pang'onopang'ono. Mu masiteji lotsiriza la matenda anati amgwirizano ziwalo.

Banja chonsechi paraplegia n'kofunika kusiyanitsa pakati otchedwa maganizo msana wa ofoola ziwalo. M'pofunika kuganizira boma la bongo m'mimba, sphincter, pamene matenda. chidwi mu nkhani iyi, anapatsidwa mbiri wodwalayo. Pokhapokha kudutsa mayesero onse ndi mayeso akhoza zikutsimikiziridwa ndi matenda Adolph Strümpell.

chithandizo

mankhwala ochiza matenda, mankhwala amakono angapereke. Therapy yafupika ndichepe zizindikiro ndi kusintha khalidwe la moyo wodwalayo.

Odwala Kwalamulidwa mankhwala kuchepetsa pang'onopang'ono minofu kamvekedwe ( "Mydocalm" "Baclofen", "Izoprotan"), asamakhale ndi nkhawa ( "Sibazon", "Nozepam", "hlozepida"), mavitamini a gulu B.

Odwala matenda izi zikusonyeza physiotherapy, paini osambira, paraffin osambira pa miyendo m'munsi. Komanso, zotsatira zabwino Tingaone pambuyo kutema mphini, acupressure ndi thupi mankhwala Inde.

mankhwala mafupa zikusonyeza ntchito orthosis wapadera, zomwe zimathandiza munthu muziyendayenda.

Nkofunika kudziwa kuti pa nkhani iliyonse, njira ya mankhwala ndi njira kugwirizana amapatsidwa payekha. dokotala ayenera kuganizira osati zotsatira za kafukufukuyu, koma mkhalidwe onse wodwala, popereka zizindikiro matenda ndi kukhalapo kwa matenda ena. Patsogolo kuperekedwa kusankha mankhwala osavomerezeka ndi kuwatsatira mosamalitsa mu mlingo kutchula. Apo ayi, kumachititsa wa madokotala ananena zawo osauka.

Adolph Strümpell matenda - ndi kudwala zovuta kwa mfundo maganizo view. Ndipo achibale ayenera kupereka zonse thandizo abwino. Maphunziro pamwamba mankhwala symptomatic bwino kutenga osachepera kawiri pa chaka. Ndi zonse ndi chokwanira chithandizo cha kudwala matendawa n'zotheka m'mbuyo. Izi zikutanthauza kuti munthu akhoza kukhala ndi moyo wabwino ngakhale ntchito kwa nthawi yaitali.

Zovuta ndi zotsatira

matenda Adolph Strümpell n'koopsa chifukwa chithunzi matenda. Munthu matenda amenewa posapita nthawi anataya mphamvu yake kusuntha kwathunthu popanda thandizo. Komanso, matendawa amakhudza ntchito anatengera kwa kutchulidwa ubongo chilema zachilengedwe kufooka minofu mwendo. Chifukwa, odwala ntchito pang'onopang'ono kusasangalala ndi moyo. Choncho anthu thandizo osati kwa akatswiri apadera, komanso zamaganizo.

zodzitetezera

mankhwala amakono simungathe, mwatsoka, kupereka njira chokwanira cha kupewa matenda, lotchedwa zifukwa zazikulu zikamera ake.

Komano, akatswiri amakhulupirira kuti tiziyesetsa kukhalabe ndi moyo zolondola, moyenera chakudya, kupereka mmalo zakudya wathanzi, musasute. Sports firming zimakhudzanso thupi lonse. Ngati achibale ndi mbiri ya matenda Adolph Strümpell, ndi bwino kukaonana pa nkhani imeneyi ndi dokotala anu ndipo ngati n'koyenera, kangapo chaka pochitika kufufuza zonse. Chotero njira sakanati yake yekha azindikire kuvutika, komanso kukhwimitsa onse kuchepetsa kupitilira ake.

Pomaliza

M'nkhaniyi, tinakambirana za chiyani Adolph Strümpell matenda. Photo odwala ndi matenda izi zikhoza kupezeka mu mabuku apadera zachipatala pakuyenerera. Kumene, kudwala izi amafuna osati njira aluso chithandizo, komanso zonse thandizo abwino kwa banja.

Asayansi padziko lonse kupitiriza mwachangu kuphunzira matenda, zimayambitsa zakuya ndi chitukuko cha mankhwala okwanira. Kale, ena amanena pa jini wapadera ndi masinthidwe, lomwe likukhudza maonekedwe a matenda.

Tikukhulupirira kuti mudziwe onse operekedwa apa adzakhala inu kwenikweni kukhala zothandiza. Khalani wathanzi!