Klippel-Trenaunay syndrome: chithunzi, zizindikiro, chithandizo

More kuchuluka matenda anapanga embryonic nthawi. Choncho, zotsatira pa chitukuko simungathe nthawi zonse. Ndipotu, ambiri a kuvutika awa amapezeka pambuyo pa kubadwa kwa mwana. Ndipo patapita kwambiri. Kuti amodzi mwa matenda majini pazikhalanso matenda Klippel-Trenaunay. Matendawa anapeza m'zaka za m'ma 20. Izi zimachitika zikamera wa sayansi ya chibadwa. Kawirikawiri matenda atengeke amuna. Komabe, Ndiponso anaona anthu wamkazi. Kudwala zimachitika matenda obadwa nawo mtima.

syndrome, Klippel-Trenaunay Kufotokozera

syndrome Klippel-Trenaunay imatengedwa ndi osowa majini chilema. Kuneneratu chitukuko cha kudwala ili pafupi zosatheka, chifukwa chilemacho kawirikawiri ndi si matenda pa mimba. Komabe, nthawi zina, matenda akhoza amaganiziridwa Klippel-Trenaunay. syndrome akutchula matenda otengera kwa makolo. Choncho, kusanthula majini ayenera kukhala pansi amayi apakati m'banja kumene matenda a matenda izi zinachitika. dzina lina matendawa - hypertrophic hemangiectasia. The matenda chithunzi Klippel-Trenaunay syndrome zikuphatikizapo zizindikiro zazikulu zitatu:

1. Varicose mitsempha.
2. Maonekedwe a mawanga zaka pa khungu.
3. Kusintha m'lifupi ndipo kutalika kwa nthambi akhudzidwa.

Nthawi zina za chigoba ndi zofewa minofu hypertrophy unkachitika. Nthawi zambiri kudwala yodziwika ndi njira patsogolo. Kuti madokotala ananena zawo zimadalira kukula kwa kusintha mtima. Ngakhale chifukwa cha matenda sangathe kuchotsedwa, mitsuko achire kuthandiza kuwongolera moyo wa wodwalayo. Anthu odwala matenda anatuma chilema.

Zimayambitsa matenda Klippel-Trenaunay

Pazifukwa zina, pali matenda Klippel-Trenaunay? syndrome akufotokozera chifukwa cha chilema chibadwa. anomaly Izi imafalikira mu autosomal lalikulu mtundu cholowa. Izi zikutanthauza kuti ngati pali chilema maselo a kholo limodzi, pali kuthekera kwa syndrome mwana ndi 50%. Komanso, matenda imafalikiranso kudzera m'badwo m'modzi, ndiye - kuchokera kwa agogo. Pankhaniyi, Mwina ndi 25%.

Monga kuvutika zonse chibadwa, kupunduka mtima kukhala pa yoopsa minofu Bookmark. Izo zikhoza bwanji mavuto aakulu. Zikuphatikizapo zinthu monga:

1. Psychological kusapeza choyamba masabata angapo mimba.
2. matenda opatsirana. Chofunika kwambiri ndi aakulu zotupa tizilombo za thupi.
3. Kugwiritsa ntchito mankhwala ndi katundu teratogenic.
4. mankhwala chikuonetseratu patangotsala mimba ndi pa mimba.
5. Kusuta ndi uchidakwa.
6. Kuwonongeka kwa mpweya ndi poizoni, cheza.

Zonsezi zingachititse kusintha mu thupi la akazi ndi mwana wosabadwa. Iwo ndi oopsa kwambiri mu magawo oyambirira mimba. Pambuyo anomalies zosiyanasiyana kwaiye mu nthawi ino.

Limagwirira a matenda

Chifukwa pali kusintha mtima matenda Klippel-Trenaunay? Matendawa amasonyezera zizindikiro za matenda venous. Limagwirira chitukuko cha kudwala ndi kutsekereza outflow magazi malekezero m'munsi. Ichi ndi chifukwa chakuti lumen venous ndi mwapang'ono, pali psinjika za wolumikizira nthambi chotengera hypertrophied minofu, yotsalira embryonic minofu. Chifukwa chophwanya wa outflow magazi pali matenda oopsa. Vienna pang'ono ndi pang'ono thinned, ongoyendayenda kuwonongeka. Komanso, akusokoneza ntchito zida valavu. Chifukwa stasis magazi nthambi akuyamba hypertrophy. Chifukwa stagnation zowawa ntchito trophic. Choncho, minofu poyera kuti ischemia. Yaitali chosokoneza a kapezedwe magazi kumabweretsa sclerosis. Zofewa minofu hypertrophy amapezeka hyperemia ndi edema. Nthawi zina, muli nkhani kusintha ndi mafupa. Choncho kwambiri ndi chiwalo mwina osati kuwonjezera m'lifupi komanso kutalika.

Klippel Trenaunay Syndrome-: zizindikiro

Ndi maonekedwe a syndrome Klippel-Trenaunay monga kusintha osati pa mbali ya dongosolo venous, koma zopindika ena. Ngakhale kuti kobadwa nako chosayenerera, zizindikiro poyamba angaoneke mu unyamata kapena mukadzakula. Choncho, mawonetseredwe matenda zikuphatikizapo kuyan'anila zotsatirazi:

1. Dilation ya mitsempha zachiphamaso mwendo. Kumaonetsa pathological kinking ndi ululu pamodzi chotengera kuonekera kwa apoyera. Nthawi zambiri varicose mitsempha yomwe ili pamwamba kunja kwa miyendo.
2. Kuwonjezeka kuchuluka kwa nthambi. Kawirikawiri limodzi ndi zochitika yotupa. Chifukwa stasis magazi anakhudzidwa mwendo angakhale osiyana kwambiri ndi nthambi wathanzi. Nthawi zambiri hyperemic, unakhuthala khungu.
3. Ziwalo kutalikitsa. Hypertrophy mungathe mapazi ndi manja.
4. Maonekedwe a nevi inki pa khungu. Mu njira ina, formations zimenezi zimatchedwa "Madontho vinyo".

Komanso kupitirira kwa matenda kuoneka kusintha trophic. zopindika anam'peza angayambe m'madera okhudzidwa, amene sindimachiritsa kwa nthawi yaitali. Pakati kuvutika ena osauka kudwala, pali polydactyly, pamaso pa zinaphatikizidwa zala inakula kapena zala.

Kodi matenda ya matenda Klippel-Trenaunay?

Syndrome matenda a Klippel-Trenaunay nthawi zambiri zochokera mawonetseredwe matenda. Zizindikiro za matenda kuoneka pang'onopang'ono. Chizindikiro choyamba kungakhale maonekedwe a "Madontho vinyo" kapena mitsempha. Ngati zizindikiro zimenezi amaphatikizidwa ndi hypertrophy chiwalo poyera matenda: Klippel-Trenaunay syndrome. Photos wa anthu odwala matenda ofanana ndi mzake. Iwo Tingaone mabuku zoyenera pathologies osowa chibadwa. Choncho, matenda ambiri sikovuta.

Kuwonjezera deta matenda, anachita venography, ultrasonography ya nthambi m'munsi, X-ray.

Klippel Trenaunay Syndrome-: mankhwala a matenda

opaleshoni imatengedwa phwando lalikulu zachipatala. Voliyumu ya alowererepo anatsimikiza ndi mlingo wa chotupa mtima. Kukuza lumen wa mtsempha stenting imagwiridwa. Pamene lalikulu chiwonongeko umabala kulambalala chotengera - n'kubweretsa ndi analili malo.

Pofuna varicose yoikidwiratu skleroteropiya, laser coagulation ya mitsempha. Odwala matenda matenda ayenera kuvala psinjika kabudula.

syndrome, Klippel-Trenaunay Kuteteza

Klippel-Trenaunay syndrome makanda sikawirikawiri matenda. Kawirikawiri izo wapezeka mu miyezi woyamba kapena moyo. Pofuna kupewa matenda, m'pofunika kudziteteza ku mavuto pa mimba. muyeso wina njira imatengedwa kuti tinafotokoza majini a mwana wosabadwayo pamaso pa milandu matenda m'banja.