Matenda Rasmussen a (encephalitis). Zifukwa Rasmussen syndrome

matenda Rasmussen ni wa gulu la matenda osowa yotupa ikufalikira mu ubongo. encephalitis kawirikawiri amapezeka ana osaposa zaka 15. Nthawi zambiri, matenda amawapeza mu zoyambira. Mu achinyamata komanso akuluakulu, mtundu uwu encephalitis chosowa kwambiri.

ndondomeko likukhudza mfundo imodzi kapena Chigawo ena a ubongo. Monga matenda ili m'kati, madokotala anazindikira kuti mwapang'onopang'ono manja. Madokotala amanenanso za kukana kwambiri mankhwala matenda. Ndipotu Rasmussen matenda - encephalitis ndi zinthu zapadera zimene sangathe anawachiritsa.

zimayambitsa Nkosatheka encephalitis Rasmussen

Mpaka etiology cha matenda osati akhazikitsidwa. Asayansi yekha tinakambirana zinthu zitatu zimene angathe kuyambitsa komanso azikhala kupitirira chikhalidwe pathological akuwuka mu chapakati mantha dongosolo. A kuchuluka kwa madokotala ndikukhulupirira kuti syndrome Rasmussen chifukwa cha chitetezo autoimmune mavairasi ndi cytotoxic T-lymphocytes.

N'zotheka udindo wa cytomegalovirus, amene anali olekanitsidwa ndi kotekisi oziziritsa odwala wamkulu. N'zotheka kuti tizilombo toyambitsa matenda amenewa chifukwa kutupa, kukulitsa matenda osachiritsika. Komanso akhoza woterowu mavuto linaonekera matenda asanayambe.

Tsopano, asayansi ambiri amakhulupirira kuti ndi chitetezo autoimmune chifukwa encephalitis Rasmussen. Zimayambitsa matenda ndi ankakhulupiriranso kuti zinakhalako cytotoxic T-lymphocytes.

Mu odwala matenda Rasmussen, ndipo nthawi zina amapezeka pakati pa abale amene amadwala matenda ena autoimmune. Mwachitsanzo, matenda Behçet a. Izi amanena amanena kuti achibale nawo pathological ndondomeko wamba mbali chibadwa. Kwenikweni, anatchula zinthu monga HLA-galotipy.

Symptomatology entsifalita Rasmussen

Poyamba, matenda kuwawonetsera focal galimoto khunyu. Nthenda matenda alowe myoclonus m'deralo. M'kupita kwa nthawi, kuukira itakula. Iwo limodzi ndi spasms minofu, imfa ya chikumbumtima ndi kugwa. Nthawi zambiri, odwala anakumana ndi kuukira akagona.

Kukula, matenda kumaonekera imfa ya mphamvu ndi tsankho dzanzi kunachitika gawo lililonse la thupi. Kafukufuku akusonyeza kuchepa ntchito mu zinkakhala m'dera ubongo.

diagnostics

Zizindikiro kutchulidwa anthu akuvutika kwa chaka ndi matenda a Rasmussen. Encephalitis ndi etiology wa Pofuna kuzindikira mwamsanga. Zimenezi zimatithandiza chiyembekezo cha zotsatira zabwino mankhwala immunosuppressive. Motero anayamba kuphunzira matenda, Kujambula ndi akugwirira imagwiridwa.

Njira zochizira encephalitis Rasmussen a

Chifukwa mpaka pali mikangano za zimayambitsa matenda Rasmussen, ndipo encephalitis osati kuchizidwa njira zinazi. Ngati kuzindikira mwamsanga matenda mankhwala antiepileptic mankhwala khalidwe. Amalangiza zakudya cholinga chake ndi kulimbikitsa mowa zakudya zamafuta, ndi kuchepetsa kuchuluka kwa chakudya zakudya zokhala ndi chakudya. Sangapeze zothandiza ntchito plasmapheresis, corticosteroids, immunoglobulins.

Nthawi zambiri, chithandizo cha matenda ayamba njira kwakukulu. Odwala amene akuvutika ndi matenda aakulu ndi zovuta choipa ubongo, m'pofunika kuchita kupatsa maselo mitsempha. Tsopano kutali zedi ife tiyesera kuchita craniotomy.

Nthawi zina odwala anapereka alowererepo opaleshoni - Hemispherectomy. Pambuyo mosavuta matenda Rasmussen a. Encephalitis, ndithudi, masamba kuda ake, kutchulidwa paresis kapena mavuto ndi kulankhula. Komabe, akuukira mtima sakhala wamba.

Kusiya opaleshoni si zofunika, ngakhale kuti sichichititsa kumaliza machiritso. Ndipotu chitukuko cha matenda kukuwonjezera kulimbikira ubongo kuchepekedwa, imene pali retardation maganizo ndi ziwalo.

Nthawi ya zotupa amgwirizano ubongo (hemispheres onse) kuneneratu mwatsoka akumane. Milandu imfa pakati pa anthu odwala ndi encephalitis Rasmussen si zachilendo.