Sideroblastic magazi m'thupi: zizindikiro, chithandizo

Anthu ambiri akudziwa kuti magazi ndi matenda oopsa kwambiri. Pali mitundu yosiyanasiyana ya matenda, ndipo aliyense wa iwo ndi zoipa thanzi la munthu. Sideroblastic magazi m'thupi ndi kudwala oopsa kugwirizana ndi makutu microelements kaphatikizidwe. Mu matenda a mafupa ntchito chitsulo kwa hemoglobin kucheza, kotero waikamo mwa ziwalo. Chinthu chachikulu - kupewa mavuto, ndipo chifukwa cha ichi tiyenera yomweyo kupempha thandizo la dokotala.

maganizo

Sideroblastic magazi m'thupi isiyana ndi zina ndende matenda yafupika wa chitsulo ndi maselo ofiira. chakuti mafupa sagwiritsa ntchito chinthu ichi mu kaphatikizidwe wa hemoglobin. Nthawi zambiri, matenda akufotokozera monga kobadwa nako kapena kugula. Pa mlingo chibadwa, magazi m'thupi kumachitika makamaka anyamata.

Matendawa akhoza opatsirana monga autosomal njira lalikulu. Zimenezi zimatchedwa magazi m'thupi syndrome Pearson. Pamene thupi bwino chosakanikirana chitsulo, ndi waikamo mwa ziwalo, chifukwa mu magazi m'thupi sideroblastic. Ngati England akukhala kwambiri, ntchito wasweka chiwindi, impso ndi minofu mtima.

mitundu ya matenda

Mtundu wa magazi m'thupi lagawidwa ndi mlingo wa mwamphamvu, komanso chifukwa cha maonekedwe ndi chithunzi matenda. mitundu yambiri yosiyanasiyana ya magazi m'thupi sideroblastic:

1. Kumtundu. Matendawo tinatengera chifukwa cha kusintha jini. Izi zimayambitsa anomaly kudwala kagayidwe kachakudya ndondomeko yokhudza vitamini B6 acid aminolevulinic. Matendawa amapangitsa lokha anamva atangobadwa kapena pa unyamata wake.
2. Kobadwa nako. mawonekedwe n'kopanda payokha, ngakhale kumlingo limakhudza mawonekedwe cholowa. Apa, yodziwika ndi okhutira mkulu wa erythrocyte coproporphyrin.
3. Waphunzira. Zikuoneka chifukwa cha mavuto mankhwala. Ena mwa iwo ndi Mowa, kutsogolera tsiklosirin.

Mavuto ndi kaphatikizidwe chitsulo kudzali chifukwa njira chotupa m'thupi. Pafupifupi 1/10 odwala ndi magazi m'thupi sideroblastic amadwala khansa pachimake.

Zimayambitsa matenda

Wochititsa matenda ndi kusowa protoporfiirina, lomwe ndi limodzi mwa zigawo zikuluzikulu zofunika kwambiri kaphatikizidwe wa hemoglobin amafotokozera. Komanso, zinthu zotani pa chilengedwe cha mapuloteni ndi chitsulo.

Kuthi mawonekedwe sideroblastic magazi m'thupi ukapezeka chifukwa chakuti thupi samalowa zinthu zofunika ndalama yokwanira. Pali zinthu kumene pawiri anakhumba ndi kuponderezedwa ndi mankhwala kuti amatenga anthu.

thupi zatha chifukwa cha kukhudzana ndi mowa. Magazi m'thupi kumachitika chifukwa poyizoni kutsogolera kapena phwando la mankhwala amphamvu. Mawonekedwe cholowa ali anadutsa wamkazi khromozomu kuonongeka matupi athu. Komanso, chifukwa cha matenda angakhale matenda chitetezo cha m'thupi ndi chitukuko cha njira neoplastic.

Matendawa sideroblastic magazi m'thupi

The ndondomeko kuzindikira matenda ndi zovuta kwambiri, chifukwa atuluka pafupifupi asymptomatic. Komanso, pali osiyana matenda chithunzi, zomwe mungathe kudalira. Ngati inu lokha pa zizindikiro zakunja matenda a matenda ndi zonama. Komabe, pali njira imodzi kudziwa sideroblastic magazi m'thupi - atayezetsa.

Komanso amachita Kupenda ziwalo za wodwalayo, kupeza madipoziti chitsulo. Koma ndi zinthu nthawi, ndipo amachititsa zizindikiro hematological. Kupewa, m'pofunika kuti atsimikizire matenda. Izi zachitika mothandizidwa ndi phunziro macroscopic a m'mafupa.

Kuti chiopsezo ndi sanamvere, m'pofunika kuchititsa biopsy. Ndi njirayi ndi njira yabwino kwambiri kudziwa sideroblastic magazi m'thupi. Iwo ikuchitika motere: chisanadze othimbirira biopsy wapadera mankhwala, ndipo ngati wapezeka chitsulo si apanga, nthumwi mankhwala kukhala kuwoneka.

Zimene katswiri kuthana?

Monga tanenera kale, zizindikiro za kuchepa magazi sideroblastic pafupifupi zotsimikizika. Chithunzi matenda nawonso akusowa, ndi chifukwa cha kuti pali mavuto ena. Ngati munthu akuona kutopa, kufooka m'thupi, izo kawirikawiri amatanthauza madokotala a. A dokotala kwa amaganiziridwa magazi m'thupi patsogolo wodwalayo ndi panthawiyi, dokotala amene kafukufuku.

Choyamba, katswiri wina wapeza ambiri boma la wodwalayo chidwi moyo, zizolowezi zoipa, mndandanda wa matenda ndi kulephereka kwa T. D. Ngati dokotala wafuna, adzakangamira maphunziro angapo. Njirazi ndi monga:

• magazi (ndi amuzolengedwa);
• chiwindi biopsy;
• kusanthula mafupa selo zikuchokera.

Panthawiyi, dokotala akhoza optionally kutsogolera wodwalayo akatswiri ena kuti tinafotokoza kokwanira kwambiri. Mwachitsanzo, kupeza mawonekedwe a magazi m'thupi, m'pofunika kutembenukira kwa chibadwa. dokotalayu adzaona ngati pali kukhala cholowa mawonekedwe a magazi m'thupi sideroblastic. Lusoli kufunsa munthu gynecologist, urologist kapena proctologist.

Njira zochizira

Musanayambe chithandizo, muyenera kudziwa ngati kulidi chitsulo mafunsidwe. Chifukwa chaichi, desferalovuyu nyemba. Iwo kutumikiridwa jekeseni mu mnofu, ndi mkodzo chifukwa ayenera allocated pafupifupi 0.5-1.1 mg wa chitsulo, ndi pa hypochromic, gipersideremicheskoy, sideroahrestical, sideroblastic magazi m'thupi - 5,10 mg.

Dziwani kuti cholowa mawonekedwe a matenda sangakhoze anachiritsidwa. Kupondereza jini amene anayamba mutate chithandizo kambirimbiri ndi mlingo waukulu wa vitamini B6. Iwo kutumikiridwa mu kuchuluka kwa mg wa 100 patsiku. Komabe, zimene thupi pafupifupi sizimadziwika. Mankhwalawa sideroblastic magazi m'thupi hemoglobin kuuka kwa milingo bwinobwino pakangotha miyezi itatu. Ngati pa nthawi ino si kuthandiza, mopitirira achabechabe mankhwala.

Kupewa ndi madokotala ananena zawo

Nthawi zambiri, matenda kumachitika chifukwa cha poyizoni patsogolo. Pofuna kupewa izi, chisamaliro ayenera kumwedwa pankhani. Pa kumanganso nyumba yakale ayenera kusamalitsa kuti adzapezekepo mongoyembekezera asamukire ana. Musati kutaya kapena m'manda utoto okhala patsogolo. Ndi bwino kuti scrape kapena kuwachotsa mankhwala. Komanso, kufunika zonse kuyan'ana ukhondo wa malo, mogwirizana ndi nyumba ndi thanzi mfundo.

Chiritsani cholowa mtundu wa matenda ndi zosatheka. Pofuna phindu ayenera nthawi zonse kuwunika udindo magazi, makamaka mlingo wa hemoglobin. Izi zimatheka ndi ndime zonse za moyo mankhwala amene salola matenda kukulitsa ndi kupitiriza chikhalidwe wabwinobwino wa munthu.