Thanzi, Khansa
Pseudomyxoma peritoneum: Zoyambitsa, Zizindikiro, Matendawa ndi Chithandizo
Pseudomyxoma peritoneum ndi kudwala kuti ndi khalidwe la kudzikundikira ntchofu, kenako likufa ziŵalo.
Kodi zikutanthauza chiyani?
A akuti anayamba ndi asayansi Werth mu 1884. Poyamba ntchito milandu zotupa sekondale, cysts chikwiyire yojambula. M'kupita kwa nthawi, ife tinapeza kuti pseudomyxoma peritoneum amachititsa kusamutsidwa mu M'mimbamo zinthu zopezeka kumapeto, amene nawonso, amakwiya yojambula mkodzo otaya kapena ndulu.
Asayansi apeza kuti kulamulira kwa ntchofu chifukwa yopuma mowiriza pamene kwambiri anatambasula kapena kuchepetsa mpanda wake makulidwe, komanso alowererepo opaleshoni: kuchotsa chotupa kapena zakumapeto.
Ndipo pansi maso pa?
Tikamaphunzira M'mimbamo pa magnification mkulu izo Tingaone kuti pseudomyxoma peritoneum wodzazidwa serous choyambirira mankhwala limene kuthandizapo ntchofu. Izi akapsa kutupa, chifukwa chimene mpanda wa mapindikidwe kumachitika:
- thickening;
- ngalande;
- makwinya.
Nthawi zina, pamwamba limakhala veleveti ngati, pamene m'madera ena pali kukha magazi. Pamene chitukuko cha kudwala amapezeka soldering matumbo zingwe zopota, omentum ndi m'mimba. Matupi kutaya koyenera kuti lidzigwira ntchito za masiku onse kuyenda.
Kuphunzira zinkakhala m'dera pansi maso, mungathe kuona kuti maselo kumene ntchofu ali ndi nsalu wosanjikiza, gawo limene pali kusalola. Epithelium ku maselo amenewa kusinthidwa kungakhale:
- kiyubiki;
- flattened.
The zikuchokera kenako maselo matenda anakhudzidwa zikusintha, amaonekera ndi siteji ya matenda. Pamene matenda a "pseudomyxoma peritoneum" maselo a ntchofu amaoneka:
- lymphocytes;
- fibroblasts;
- Mipikisano pakati Arefai;
- polymorphic leukocytes;
- histiocytes;
- columnar epithelium.
The njira yamasika anapatsa peritoneum lapansi. Iwo likulowerera mu thupi izo kupyolera perforation lapansi. Ndi chifukwa cha kuchuluka kwa epithelium, ndipo m'gulu gulu la neoplastic matenda pseudomyxoma peritoneum, amene zizindikiro zambiri zoonekeratu. Dongosololi atuluka sluggishly, mothandizidwa ndi ntchofu, akuti ndi yotupa.
chotupa A - ndi mantha?
Zotupa secrete peritoneum mitundu iwiri:
- chachikulu;
- sekondale.
Wa mankhwala zilonda zambiri atakhazikitsa izo metastatic, kuti ndi sekondale. Koma chachikulu, ndiye kuti muli pseudomyxoma peritoneum. Zizindikiro za matenda kwa nthawi yoyamba, ndi wosaoneka. Ndi chitukuko cha maselo matenda kufala amapezeka padziko peritoneal popanda okhudza ziwalo pafupi. Iyi ndi mbali yofunika kwambiri ya khansa anafotokoza. Njira ya maselo kafalitsidwe matenda - akakufunsani.
Zikatero, kupatula pamene England adabwa ndi zina nsalu, kunena matenda pseudomyxoma peritoneum, amene Mapa ndi zovuta. Izi zimadalira chifukwa chakuti kudwala nthawi wapezeka mu maziko a khansa kale kale anati ziwalo zina.
diagnostics
Matendawa "pseudomyxoma peritoneum" nthawi anaika laparotomy. Perekani izo zizindikiro zotsatirazi:
- ululu m'mimba (zambiri kuzimiririka);
- kuonjezera buku la mmimba popanda chifukwa chenicheni.
Izi zimachitika chifukwa kudzikundikira mu zimakhala wa madzi m'thupi.
wolemekezeka:
- kuwonongeka zochepa;
- psevdomiksoglobulez.
Kodi zimenezi zimachitika?
Childs, matenda kumaonekera maziko chotupa chotupa. Ichi ndi chifukwa chakuti yojambula ndi malowedwe mu zonse m'mimba, osati amatope, komanso a epithelium lapansi. maselo wake ndi luso lapadera kuti anapatsa minofu mu wawo. M'kupita kwa nthawi, malo otsika kuyamba kubala ntchofu.
Kawirikawiri, matenda a "pseudomyxoma peritoneum" zikutanthauza kuti matenda ndi zilonda. Kudwala a pamwamba, musati kuyambitsa kuswa kugwira ntchito kwa ziwalo ndi kachitidwe. Pseudomyxoma m'manja, kuti amakhala ndi "kugwedeza syndrome". Masiku ano, yodalirika njira Kupeza Vuto matenda - opaleshoni imene zitsanzo minofu analandira. kudwala chitsimikiziro amaperekedwa ndi biopsy a.
Tiyembekezere zotani?
Muyenera kukhala okonzeka kuonetsetsa kuti matenda "pseudomyxoma peritoneum" mankhwala - opaleshoni. Njira ina yabwino kuthana ndi kudwala koma anatulukira sanali. Ngati mtima wabwino chotupa, izo kudula, anapatsidwa kumene minofu adakali wathanzi.
Pamene matenda alibe yekha kulandira mwayi zilonda mankhwala, amene ali okonzeka kupita kuchotsa kwakukulu. Kuti madokotala ananena zawo ndi zovuta. kuchira Full tingayembekezere pa nkhani ya mtima wabwino chotupa kwa ndondomekoyi, koma pambuyo kusinthika ngakhale opaleshoni sangathe kwathunthu kutchinga njira yopanga ndi kudzikundikira amatope.
Madokotala si nthawi zonse amatha molondola kuona ngati panali kale chotupa chija. Ichi chavumbulutsidwa mu phunziro histological, zomwe zingasonyeze pakalibe maselo a khansa mu minofu chitsanzo adzatengedwa, koma sangathe kutumikira monga chitsimikizo chakuti m'thupi palibe konse.
Pamene matenda "pseudomyxoma peritoneum" chithandizo amusankha, poganiza kuti chotupa kale chotupa chija. Ichi ndi chifukwa pafupipafupi mkulu wa kumwa, kuwukira.
Kodi kuchita?
Musanayambe kumvetsa zimene matenda "pseudomyxoma peritoneum" (gawo lotsiriza) zizindikiro za matenda, choyamba kufunika kulongosolerana, cheza mankhwala ndi mankhwala anasonyeza inefficiency polimbana ndi matenda.
Panthawi pano, osati anatulukira chapadera matenda. Mwachidule kuchotsa mamina anasonyeza inconclusive chifukwa maselo kuloŵa epithelium, pitirizani kuzichita izo.
Akukhulupirira kuti zotsatira zabwino chingapezeke mwa radiotherapy, pamene pali padzuwa la zimakhala bwanji ndi pulatinamu, isotopes golide.
Popanda mankhwala olondola a munthu wodwala afa mu zaka imodzi kapena ziwiri. Nthawi zina, matenda limodzi ndi fistula pakhungu.
zina zabwino zofunika
Ziwerengero kuti pseudomyxoma peritoneum amapezeka pafupifupi 1% odwala Choncho, zimagawidwa monga yosowa kwambiri. kuopsa kwake ndi utuluke chobisika, chitukuko atypical, ndi madokotala ananena zawo osauka.
Nthawi zina, chitukuko cha kudwala amapezeka ndi mucin appendicular. Mwa zizindikiro likunena za Oncology - matumbo kutsekeka.
Matendawa ali ndi makhalidwe a mitundu zotsatirazi mucin:
- Free.
- Madipoziti. Kuonetsetsa lalikulu, ang'onoang'ono. Iwo wokongola zolimba zoyenera pamwamba peritoneal. Madipoziti zimachitika njira yotupa ndi alipo mesothelial maselo. Nthawi zina, pali fibroblasts, capillaries. Koma maselo sanali pulasitiki nthawi zambiri sichingapezeke.
- Pools. misa Awa ndi zambiri monga minofu chipolopolo kollagenizovannuyu. Mu maphunziro sayansi, monga komanso yogawanika ya mucin.
Amene amakhulupirira?
M'zaka zaposachedwapa, zipatala zingapo Israeli kuonetsetsa mankhwala kwathunthu ndi khansa. Childs, mabungwe amenewa musataye malonjezo aliwonse boma koma kupanga catchy malonda, kupereka chiyembekezo kwa odwala ndi achibale awo.
Kumbukirani kuti muyenera kusankha mabungwe zachipatala, poyamba m'mene ankaphunzira zolembedwa za, komanso mayankho a anthu amene anapita kumeneko chithandizo. Chenjerani ndi madokotala oipa ndi utumiki osauka.
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