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Myasthenia gravis: ndichiyani? Zoyambitsa, Zizindikiro ndi Njira Chithandizo

Myasthenia amatchedwa matenda amene anatsagana ndi kuchuluka kufooka minofu. A matenda ofanana anafotokozedwa koyamba mu 1672. Malinga ndi kafukufuku, matenda zimachokeradi nthawi zambiri. Komabe, anthu ambiri amachita chidwi ndi mafunso okhudza chifukwa pali mwamuna, ndichiyani ndi zizindikiro namtsata. Ndipotu, matenda oyambirira zimatengera kamwedwe ndi khalidwe la moyo wa munthu wodwalayo.

Myasthenia gravis - ndichiyani? The zimayambitsa matenda

Ngati chirichonse yachibadwa acetylcholine pa malemeredwe alowa mphanga synaptic, amene amachita pa maselo apadera Kakhungu minofu - motero ndi analimbikitsa ndi kuchepetsa ulusi minofu. Koma makanda, limagwirira ichi cha kufala kwa mitsempha mopupuluma wathyoka.

Mwakucimbidza Dziwani kuti myasthenia gravis - matenda chibadwa. Ndipo lero anaganiza kuonetsetsa njira ziwiri zoyambirira za chitukuko. Nthawi zina, kulephera kufala kwa mopupuluma mitsempha amagwirizana ndi kusokonezeka kwa chamoyo yachibadwa ya ubongo imene imalamulira kutentha kwa. Wina chifukwa chofala cha matenda ndi chotupa autoimmune wa thymus England, imbaenda kuchepetsa kuchuluka apanga acetylcholine.

Pali otchedwa neonatal myasthenia gravis. Ndi chiyani icho? Izi mawonekedwe a matenda amapezeka akhanda ngati mai awo akudwala matenda a conduction neuromuscular.

Zizindikiro za matenda angasonyeze monga m'masiku oyambirira atabadwa, ndipo wamkulu kwambiri. Pali zina zothandizira nthendayi kuti chingachititse myasthenia osauka gravis. The zifukwa kuukira kufooka minofu kungakhale chifukwa nkhawa kwambiri, nkhawa mantha, matenda akale opatsirana ndi matenda a chitetezo cha m'thupi.

Zizindikiro zazikulu za myasthenia gravis

Monga tanenera kale, mbali yaikulu ya matenda ndi minofu kufooka. M'mawa, odwala zambiri mumamva n'kwachibadwa. Koma maola angapo minofu chigoba asatope ndiponso kusiya kugwira ntchito mpaka kupheratu ziwalo. Tinakhalako luso kuchepetsa anachira.

Malinga ndi gulu anakhudzidwa misempha lagawidwa njira zitatu za matendawa:

  • Nthawi zambiri matendawa amakhudza minofu, amene innervated ndi misempha cranial. Ndipo mbali yaikulu mu nkhani iyi ndi ptosis. Ngati munthu akhoza mpumulo kwathunthu kutsegula maso anu, ndiye pambuyo maola angapo, pali kuŵeramitsa mwapang'onopang'ono zikope chapamwamba.
  • Palinso bulbar myasthenia gravis. Ndi chiyani icho? matenda limodzi ndi kuswa mitsempha mopupuluma kufala kwa minofu, amene ali ndi udindo mu kumeza kutafuna ndi ena njira zina. Odwala a anthu mavuto ndi kudya, komanso kusintha mawu, mpaka mofulumira yake.
  • Mu mawonekedwe ambiri zowombetsa mkota wa matenda amawapeza, imene minofu diso amakhudzidwa choyamba, ndiye ndondomeko atuluka m'khosi, m'makona chapamwamba, ndi zina zotero D..

Njira ya chithandizo cha myasthenia

Dziwani kuti matenda myasthenia gravis ndi woopsa kwambiri ndipo amafuna chisamaliro aluso. mfundo ndi yakuti matenda amakhala ndi mavuto otchedwa, amene anatsagana ndi ziwalo zosakhalitsa minofu kupuma, ndipo uyu ndi kuopseza mwachindunji moyo.

Yekha mankhwala ndi utsogoleli wa mankhwala okhala acetylcholinesterase - ndi "Proserpine" ndi "Kalimin". mankhwala amenewa yotsiriza kwa zaka, ndi mlingo wa mankhwala zikusintha malingana boma ndi mlingo wa chitukuko cha matenda. Ngati myasthenia gravis anayamba ndi maziko a chotupa cha thymus England, opaleshoni imagwiridwa kuchotsa thupi.

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