Thanzi, Matenda ndi zokwaniritsa
Eisenmenger syndrome: zizindikiro. Eisenmenger syndrome ndi mimba. Odwala matenda Eisenmenger
patsogolo kusonyezeka mankhwala m'zaka zingapo zapitazi osati kutsogoleredwa kuwonjezeka lakuthwa mu moyo amayembekezeka, kapena kuwonongedwa kwa pathologies mtima. Komanso, kumayambiriro kwa XIX-XX zaka zambiri, asayansi anafotokoza matenda ambiri atsopano. Chifukwa ena a iwo akali chinsinsi, zizindikiro - khungu, ndipo mankhwala ndi zovuta. Eisenmenger syndrome, dzina la dokotala Austria ndi cardiologist, sangatengedwe kukhala wamba. Osowa kudwala analandira nkhani pafupifupi zaka 100 zapitazo. Komabe, ngakhale masiku ano, alibe kulankhula za kumvetsa bwino etiology ake.
zambiri
Syndrome (limatchedwa zovuta) Eisenmenger - ndi kudwala choopsa kwambiri, anakafika ku m'mapapo mwanga ndi dongosolo mtima. matenda mtima wofanana ndi kuphatikiza yamitsempha yamagazi septal chilema , ndi matenda oopsa. chitukuko matenda kumayambitsa kuthamanga chinawonjezeka ndi chisokonezo kufalitsa m'mapapo mwanga. Chifukwa ndi shunt, amene ali ndi udindo kwa magazi stuffing kumanja mpaka kumanzere, amene amaswa yachibadwa njira hemodynamics.
Komanso, mfundo syndrome Eisenmenger kuphatikiza zina matenda a mtima, yodziwika ndi lotseguka atrioventricular ngalande ndi setifiketi ductus arteriosus, pamaso pa ventricle chimodzi chokha. Pakati pa odwala ndi nthenda yamitsempha yamagazi septal kudwala amawapeza 10% ya milandu. Mu dongosolo la kobadwa nako zopindika waukulu thupi minofu Eisenmenger zovuta ndi 3%.
Zimayambitsa chitukuko syndrome
zimayambitsa Single wa chitukuko cha matenda, madokotala mwina wosayesedwa. Komabe, pali zinthu zingapo etiological kuti azidwala ndi ana amene ali ndi matenda Eisenmenger:
- Cholowa chimene chingawapangitse kukhala zidakwa. Kuphwanya pa mlingo jini akhoza wadutsa kuchokera ku kholo mwana, potero kupangitsa kochulukira mwayi kudwala matenda a mtima.
- zinthu Environmental:
- Kuledzela wa mwana wosabadwayo mu utero;
- yaitali kukhudzana ndi cheza mu atomu;
- aakulu nthenda ya kholo;
- mphamvu ya mankhwala ndi zowonjezera zakudya ntchito ndi akazi pa mimba.
mfundozi sizionekaoneka basi syndrome Eisenmenger, koma chiphunzitso iwo akhoza kukhala chifukwa cha pathologies osiyanasiyana, kuphatikizapo munthu.
Monga matenda akufotokozera?
Odwala matenda Eisenmenger samasankha amadandaula matenda. Choncho, matenda oyambirira Sizotheka. Mwana woyamba amamangirira njira compensatory, koma patapita kanthawi matenda kumaonekera. chuma Internal kuotcha, dongosolo mtima akulephera. ndi Eisenmenger syndrome zizindikiro zotani?
- Kuchuluka kufooka, zoipa pambuyo thupi.
- Ululu kumanzere kwa pachifuwa.
- Kuwonjezeka blueness masana a khungu.
- Mowiriza syncope.
- Matenda chifuwa ndi kumaliseche wamagazi.
Zizindikiro oterowo nkhawa si onse ayi. The syndrome kwa nthawi yaitali angathe mofulumira. Ngati dokotala amene imayang'anira mwana, tikulimbikitsidwa pochitika kuunikidwa zina pakati cardiology, iwo ayenerabe kuwasamalira.
kuchipatala kuti akalandire chithandizo akudwala
madokotala Russian ndikukhulupirira kuti syndrome Eisenmenger ndi mimba ali osayenerana. Choncho, pa siteji iliyonse ya mkazi mimbayo bwino. anzawo Western sakuganiza. Malinga ndi iwo, mibadwo wolemera zimadalira zoletsedwa ndi malamulo ndi malangizo.
Mkazi woyamba m'chipatala kwa nyengo yonse ya mimba. Kuchipatala, madokotala ayenera nthawi zonse kuwunika udindo wa mwana wosabadwayo ndi kuyeza kuthamanga mu capillaries m'mapapo mwanga. Zizindikiro loyamba kufupika kwa mpweya - masks oxygen. Kuyambira wachiwiri trimester anatumizidwa coagulants chithandizo. A masiku pang'ono tsiku ankayembekezera zosayembekezereka wa mwana analimbikitsa mankhwala mantha a digitalis kukhalabe dongosolo mtima. Kutumiza n'chotheka mwachibadwa.
Ngati mkazi ayenera kukhala ndi zofunikira za madokotala, Mwina ziyende bwino mwanayo ndi 50-90%. The Mapa si monga abwino mayi. N'chifukwa chake posankha zochita pa nkhani yopitiriza mimbayo, mkazi ayenera kuganiza za mavuto angathe.
Kupenda Medical
mankhwala ochiza odwala matenda Eisenmenger sikutheka kulingalira popanda kufufuza wapadera. Likhoza kupita mu zipatala apadera ndi zipangizo zoyenerera. Ngati mukukayikira kuti kudwala mosamala pulogalamu ameneŵa:
- pachifuwa radiograph (kusintha kafukufuku mu mtsempha wamagazi m'mapapo mwanga ndi contours kwa mtima);
- angiography (phunziro mtima);
- ECG (kudziwa zobisika mtima mungoli chisokonezo);
- Echocardiography (zowonera kusintha pathological m'makoma ventricles a);
- mtima catheterization (ziyenera a matenda ndi chikhalidwe cha kuvulala, muyeso wa magawo n'zosangalatsa kumva za minofu yaikulu).
matenda masiyanidwe ndi kuvomerezedwa odwala onse ndi amaganiziridwa matenda Eisenmenger. Pentad Fallot, mtsempha wamagazi stenosis, setifiketi ductus arteriosus - yochepa mndandanda wa pathologies kuti achotse.
mfundo mankhwala
chithandizo ndiwofatsa odwala n'zotheka, koma si bwino. Komano, ntchito za phukusi opaleshoni sikuti ndi zotsatirapo zabwino. Choncho, lero madokotala ambiri moyembekezera strategy kuphatikiza.
Odwala ndi chithunzi kutchulidwa matenda ndi kuchuluka hematocrit yoikidwiratu phlebotomy. Ndondomeko mobwerezabwereza katatu pa chaka, pa nthawi yomweyo m'pofunika kuti aziona magawo magazi chitsulo. Mpweya mankhwala ndi anticoagulant mankhwala sikawirikawiri ntchito, m'malo okhulupirika. The drawback waukulu njira zimenezi akuti zambiri zotsatira zoyipazi, lofunika kwambiri mwa zomwe ndi hemorrhagic diathesis. Komanso, odwala Kwalamulidwa mankhwala. "Epoprostenol" ndi "Treprostinil" bwino hemodynamics ndi "Traklir" amachepetsa mtima kukana.
Opaleshoni ikuchitika mitundu iwiri: implantation wa pacemaker ndi, pulasitiki chilema MPP. Pamene Eisenmenger syndrome ntchito akhoza kwambiri bwino kuti madokotala ananena zawo za matendawa. Ngati mankhwala awa ali osamveka, likhoza kuthandiza munthawi yomweyo kupatsidwa zina za m'mapapo ndi mtima. Kupatsidwa zina opaleshoni mwapadera zovuta amafuna ndalama lalikulu ndalama. Komano, zilibe kuthetsa kufala kwa zosokonezeka. Pamene palibe njira ina, funso zinthu zolungama, awiri kumuika angapulumutse moyo. Isanafike kukhazikitsa n'kofunika pochitika kuipidwa zachipatala bwino.
Kodi odwala matenda Eisenmenger?
Anthu amene anali kulimbana ndi matenda mtima, kawirikawiri amakhala ndi moyo wokangalika. Komabe, iwo nthawi zonse kupita kwa dokotala ndi kuwunika mosavuta zizindikiro thanzi. odwala ayenera kupewa madzi m'thupi, kukhudzana yaitali kuti okwera matenda opatsirana. Nkofunika kusiya zizolowezi zoipa ndi kumwa mankhwala zomwe zingachititse magazi. Ngati wodwala motere malamulo dokotala, Mwina n'zotheka kukhala zabwinobwino ukuwonjezeka moyo. Apo ayi, magazi okusijeni amagwa kuchepetsa yovuta imene ndi imfa.
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